Perspectiva del especialista en cirugía oral y maxilofacial sobre las anomalías de la dentina centradas en la dentinogénesis imperfecta: una revisión narrativa

Karthik Shunmugavelu, Evangeline Cynthia Dhinakaran, Sravya Vemareddy, Ramadevi RP

Resumen


La dentinogénesis imperfecta se caracteriza por una baja tasa de mutación, alta penetrancia y herencia autosómica dominante. Afecta tanto a la dentición decidua como a la permanente. Una característica importante es la displasia mesodérmica, observada en la histodiferenciación. El diagnóstico precoz y el tratamiento eficaz permiten un pronóstico favorable. Este trastorno dentinario hereditario se describe detalladamente en esta revisión narrativa.

Recibido: 31-07-2025
Aceptado: 17-09-2025

 


Palabras clave


Oral; dental; dentinario; hereditario; anomalía

Texto completo:

PDF (English)

Referencias


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DOI: https://www.doi.org/10.53766/AcBio/

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